Chithandizo cha sickle cell anemia

Supplementation. Kuonjezera tsiku ndi tsiku ndi kupatsidwa folic acid (kapena vitamini B9) ndikofunikira kulimbikitsa kupanga maselo ofiira atsopano.

Hydroxyurea. Poyambirira, anali mankhwala oletsa khansa ya m'magazi, koma analinso mankhwala oyamba omwe adapezeka kuti ali othandiza pochiza matenda a sickle cell anemia kwa akuluakulu. Kuyambira m'chaka cha 1995, zadziwika kuti zimatha kuchepetsa nthawi zambiri zowawa komanso matenda a chifuwa chachikulu. Odwala omwe amagwiritsa ntchito mankhwalawa safunikiranso kuikidwa magazi.

Kuphatikiza apo, kuphatikiza kugwiritsa ntchito hydroxyurea ndi erythropoietin kungawonjezere mphamvu ya hydroxyurea. Majekeseni opangidwa ndi erythropoietin amagwiritsidwa ntchito kulimbikitsa kupanga maselo ofiira a magazi ndi kuthetsa kutopa. Komabe, ndi zochepa zomwe zimadziwika ponena za zotsatira zake za nthawi yaitali, makamaka chifukwa cha chiopsezo cha kutsika koopsa kwa maselo a magazi. Kugwiritsa ntchito kwake kwa ana omwe ali ndi matenda a sickle cell akuphunziridwabe.

Kuikidwa magazi. Mwa kuwonjezera kuchuluka kwa maselo ofiira a magazi, kuthiridwa magazi kumateteza kapena kuchiza zovuta zina za matenda a sickle cell. Kwa ana, iwo amathandiza kupewa sitiroko kubwereza ndi kukulitsa ndulu.

N'zotheka kubwereza kuikidwa magazi, ndiye kuti m'pofunika kuchiritsidwa kuti muchepetse chitsulo chamagazi.

opaleshoni

Maopaleshoni osiyanasiyana amatha kuchitika pakabuka mavuto. Mwachitsanzo, tingathe:

- Chitani mitundu ina ya zotupa za organic.

- Chotsani ndulu.

- Ikani fupa la m'chiuno pakachitika chiuno necrosis.

- Pewani zovuta zamaso.

- Pangani zomata pakhungu pochiza zilonda zam'miyendo ngati sizichira, ndi zina.

Ponena za kuyika mafupa, nthawi zina amagwiritsidwa ntchito mwa ana ena ngati ali ndi zizindikiro zoopsa kwambiri. Kuchitapo kanthu koteroko kungathe kuchiza matendawa, koma kumapereka zoopsa zambiri popanda kuganizira kufunika kopeza wopereka woyenera kuchokera kwa makolo omwewo.

NB Mankhwala angapo atsopano akuphunziridwa. Umu ndi momwe zilili makamaka ndi chithandizo cha majini, chomwe chingapangitse kuti zisagwire ntchito kapena kukonza jini yolakwika.

Popewa zovuta

Kulimbikitsa spirometer. Pofuna kupewa mavuto a m’mapapo, anthu amene ali ndi ululu waukulu m’mbuyo kapena pachifuwa angafune kugwiritsa ntchito chipangizo chotchedwa spirometer, chomwe chimawathandiza kupuma mozama.

mankhwala. Chifukwa cha kuopsa kwa matenda a pneumococcal kwa ana okhudzidwa, amapatsidwa penicillin kuyambira kubadwa mpaka zaka zisanu ndi chimodzi. Mchitidwewu wachepetsa kwambiri kufa kwa anthu amsinkhu uno. Mankhwala opha tizilombo adzagwiritsidwanso ntchito popewa matenda mwa akuluakulu.

katemera. Odwala sickle cell - ana kapena akuluakulu - ayenera kudziteteza makamaka ku chibayo, chimfine ndi chiwindi. Katemera wanthawi zonse akulimbikitsidwa kuyambira kubadwa mpaka zaka zisanu ndi chimodzi.

Pakakhala vuto lalikulu

Zopweteka. Amagwiritsidwa ntchito polimbana ndi ululu pakakhala vuto lalikulu. Malingana ndi vutolo, wodwalayo akhoza kukhutitsidwa ndi mankhwala ochepetsa ululu kapena kulembedwa amphamvu kwambiri.

Thandizo la oxygen. Pakachitika chiwopsezo chachikulu kapena zovuta za kupuma, kugwiritsa ntchito chigoba cha okosijeni kumapangitsa kupuma mosavuta.

Kutsekula m'madzi. Zikachitika zowawa, intravenous infusions ingagwiritsidwenso ntchito.

Siyani Mumakonda