dysmorphia

dysmorphia

Mawu akuti dysmorphia amatanthauza zolakwika zonse kapena kupunduka kwa ziwalo za thupi la munthu (chiwindi, chigaza, minofu, etc.). Nthawi zambiri, dysmorphia iyi imakhalapo kuyambira pakubadwa. Kungakhale chizindikiro cha matenda aakulu.

Dysmorphia, ndi chiyani?

Dysmorphia imaphatikizapo zolakwika zonse za thupi la munthu. Kuchokera ku Chigriki "dys", zovuta, ndi "morph", mawonekedwe, mawuwa amatanthauza ndendende mitundu yachilendo ya chiwalo kapena gawo lina la thupi. Ma dysmorphisms ndi ochuluka kwambiri komanso amasiyana mosiyanasiyana. Chifukwa chake, dysmorphia ingatanthauzenso kusakhala bwino kwa chiwalo mwa munthu, poyerekeza ndi anthu ena onse, ngati vuto lalikulu.

Nthawi zambiri timalankhula za dysmorphia kuti titchule:

  • Craniofacial dysmorphia
  • Hepatic dysmorphia (chiwindi)

Poyamba, dysmorphia imanenedwa kukhala yobadwa nayo, ndiko kunena kuti ilipo kuyambira kubadwa. Izi ndizochitikanso chifukwa cha malekezero a dysmorphic (chiwerengero cha zala zazikulu kuposa khumi, ziboda etc.) Ngakhale kuti dysmorphism ya chiwindi imatha kuwoneka chifukwa cha matenda a cirrhosis, kaya chiyambi chake ndi mavairasi kapena chifukwa cha mowa. 

Zimayambitsa

Pankhani ya congenital dysmorphias, zomwe zimayambitsa zimatha kukhala zosiyanasiyana. Kuwonongeka kwa nkhope nthawi zambiri kumakhala chizindikiro cha matenda, monga trisomy 21 mwachitsanzo. 

Zifukwa zitha kukhala zoyambira:

  • teratogenic kapena kunja (kumwa mowa, mankhwala osokoneza bongo kapena kukhudzana ndi mankhwala pa nthawi ya mimba etc.)
  • opatsirana kudzera mu placenta (mabakiteriya, mavairasi, majeremusi)
  • makina (kupanikizika kwa mwana wosabadwayo etc.)
  • chibadwa (chromosomal ndi trisomies 13, 18, 21, cholowa, etc.)
  • Osadziwika

Ponena za hepatic dysmorphism, mawonekedwe a malformation amachitika limodzi ndi matenda enaake. Mu kafukufuku yemwe adachitika mu 2004, wofalitsidwa mu Journal of Radiology: 76,6% mwa odwala 300 omwe adatsatiridwa ndi matenda a cirrhosis adawonetsa mtundu wina wa hepatic dysmorphism.

matenda

Matendawa nthawi zambiri amapangidwa pobadwa ndi dokotala wa ana monga gawo la kutsata kwa mwanayo. 

Kwa odwala matenda enaake, dysmorphia ndi vuto la matendawa. Dokotala adzayitanitsa CT scan.

Anthu okhudzidwa ndi zoopsa zomwe zingachitike

Cranio-Facial Dysmorphies

Kobadwa nako malformations kukhala osiyana chiyambi, iwo angakhudze onse akhanda. Komabe, pali zinthu zomwe zimawonjezera mawonekedwe a matenda kapena ma syndromes okhudza dysmorphia: 

  • kumwa mowa kapena mankhwala osokoneza bongo pa nthawi ya mimba
  • kukhudzana ndi mankhwala pa mimba
  • consanguinity
  • cholowa pathologies 

Mtengo wabanja wopangidwa ndi dokotala wa ana ndi makolo obadwa nawo pamibadwo iwiri kapena itatu ukulimbikitsidwa kuti uzindikire zomwe zimayambitsa ngozi.

Dysmorphies hepathiques

Anthu omwe ali ndi vuto la cirrhosis ayenera kuyang'anitsitsa dysmorphism.

Zizindikiro za dysmorphia

Zizindikiro za congenital dysmorphia ndizochuluka. Dokotala wa ana adzayang'anira:

Kwa nkhope ya dysmorphia

  • Maonekedwe a chigaza, kukula kwa fontanelles
  • Alopecia
  • Maonekedwe a maso ndi mtunda pakati pa maso
  • Maonekedwe ndi mgwirizano wa nsidze
  • Maonekedwe a mphuno (muzu, mlatho wamphuno, nsonga etc.)
  • The dimple pamwamba pa mlomo kuti fufutidwa mu fetal alcohol syndrome
  • Maonekedwe a mkamwa (milomo yong'ambika, makulidwe a milomo, mkamwa, uvula, mkamwa, lilime ndi mano)
  • chibwano 
  • makutu: malo, malo, kukula, hemming ndi mawonekedwe

Kwa dysmorphias ena

  • malekezero: kuchuluka kwa zala, mphuno kapena kuphatikizika kwa zala, kuphwanya kwapachala, etc.
  • khungu: zosokoneza za mtundu, mawanga a café-au-lait, ma stretch marks etc.

Chithandizo cha dysmorphia

Congenital dysmorphias sangathe kuchiritsidwa. Palibe mankhwala omwe apangidwa.

Zochitika zina za dysmorphism ndizochepa ndipo sizidzafuna chithandizo chamankhwala. Ena akhoza kuchitidwa opaleshoni kudzera mu opaleshoni; izi ndi nkhani ya cholumikizira cha zala ziwiri mwachitsanzo.

Pazovuta kwambiri za matendawa, ana adzafunika kutsagana ndi dokotala panthawi yomwe akukulirakulira, kapenanso kutsatira chithandizo chamankhwala kuti apititse patsogolo moyo wa mwanayo kapena kulimbana ndi vuto lokhudzana ndi dysmorphia.

Pewani dysmorphia

Ngakhale chiyambi cha dysmorphism sichidziwika nthawi zonse, kukhudzana ndi zoopsa pa nthawi ya mimba kumachitika nthawi zambiri. 

Choncho, ndikofunika kukumbukira kuti kumwa mowa kapena mankhwala osokoneza bongo pa nthawi ya mimba ndizoletsedwa, ngakhale pang'ono. Odwala oyembekezera ayenera nthawi zonse kukaonana ndi dokotala musanamwe mankhwala aliwonse.

Siyani Mumakonda