Kodi hemochromatosis ndi chiyani?

Kodi hemochromatosis ndi chiyani?

Hemochromatosis (yemwenso amatchedwa genetic hemochromatosis kapena heredch hemochromatosis) ndi matenda obadwa nawo obadwa nawo. kuyamwa kwambiri kwachitsulo kudzera m'matumbo ndi m'matumbo kudzikundikira mu thupi.

Zomwe zimayambitsa hemochromatosis

Hemochromatosis ndimatenda amtundu wolumikizidwa ndi a Kusintha kwa majini amodzi kapena angapo. Kusintha uku kumachitika m'malo osiyanasiyana padziko lapansi ndipo chilichonse chimafanana ndi chiwonetsero cha matendawa.

THEchithokomiro cholowa HFE (wotchedwanso mtundu wa hemochromatosis) ndiye mtundu wofala kwambiri wamatendawa. Zimagwirizanitsidwa ndi kusintha kwa jini la HFE lomwe lili pa chromosome 6.

Pafupipafupi matenda

Hemochromatosis ndi imodzi mwazofala kwambiri zamatenda amtundu.

Pafupifupi munthu m'modzi mwa anthu 1 ali ndi vuto lomwe limayambitsa matendawa1. Koma chomwe chikuyenera kumvedwa tsopano ndikuti matendawa amatha kuwonetsa kusintha kwamankhwala mosiyanasiyana kuti mitundu yayikulu ya hemochromatosis ikhale yosowa.

Anthu okhudzidwa ndi matendawa

The anthu amakhudzidwa kwambiri kuposa akazi (amuna atatu pa mkazi m'modzi).

Zizindikiro zimawoneka nthawi zambiri Zaka 40 pambuyo pake koma imatha kuyambira pakati pa 5 ndi 30 wazaka (juvenile hemochromatosis).

Matendawa amapezeka kwambiri kumadera ena padziko lapansi, mwachitsanzo ku United States kapena kumpoto kwa Europe. Sipezeka m'maiko a Southeast Asia kapena anthu akuda.

Ku France, madera ena (Brittany) amakhudzidwa kwambiri.

Siyani Mumakonda